Dermal nerve sheath myxoma is a rare benign myxoid tumor of nerve sheath origin, usually occupied in the dermis. It is usually located on head and neck or upper extremities and mainly occurs in children and young adults. It typically presents as solitary slow-growing superficial mass ranging in size from 0.5 cm to 2 cm and typically composed of well-defined lobules of the myxoid spindle to stellate cells. S-100 protein staining indicates that it is composed mainly of neoplastic Schwann cells. Because dermal nerve sheath myxoma is a benign tumor, it can be managed with local excision. A 63-year-old woman visited our clinic with 0.5 cm x 0.5 cm sized flesh to pinkish colored dome shaped nodule on the back that she noticed since two years ago. She had diabetes and had no other recognizable medical history or family history. With an impression of neuroma, excisional biopsy was performed. Histopathological examination revealed well-demarcated myxoid lobules of varying sizes, separated by fibrous septa and these cells were immunoreactive to S-100 protein. According to these findings, the lesion was diagnosed as a dermal nerve sheath myxoma. After excision, the patient has been observed without recurrence or complications. This case is noticeable in that, the disease itself is rare, and even it had occurred at an uncommon site in a patient in her sixties.