Neutrophilic urticarial dermatosis (NUD) clinically resembles urticarial but histopathologically represents a neutrophilic dermatosis. Affected patients develop erythematous macules, papules or slightly raised plaques on the skin that resolve within 24 to 48 hours. Trunk and extremity involvement is most common. Histopathologic examination of NUD reveals an intense neutrophilic infiltrate in the dermis with leukocytoclasia, but without significant edema in dermis or fibrinoid necrosis of vessel walls which is usually seen in vasculitis. Clinical manifestations of NUD are similar with urticarial but skin lesions of NUD frequently last more than 24 hours and accompany with systemic symptoms such as fever and joint pain. NUD differ from Sweet’s syndrome in terms of no lesional pain and the lesions of NUD are clinically far less edematous and raised than in Sweet’s syndrome. In histologic terms, major derma edema with a denser neutrophilic infiltrate is seen in Sweet’s syndrome than NUD. A 69-year-old female patient came to emergency room for fever and spreading erythematous patches and plaques on the face, trunk and both extremities for 1 week. Skin biopsy showed mild upper dermal edema and interstitial neutrophilic infiltrate in dermis. Direct immunofluorescence showed C3 deposition on the blood vessels. Skin lesions and fever were cleared without recurrence after the treatment of systemic corticosteroid and colchicine.