Fetal Isolated ventricular non-compaction (IVNC) of the myocardium is a very rare cardiomyopathy characterized by the persistence of prominent ventricular myocardial trabeculations and deep intertrabecular recesses with direct vascular supply by the ventricular cavities. Normally between the fetal 5th week and 8th week, intertrabecular spaces are obliterated and ventricular compaction occurs from the base towards the apex and from epicardium to endocardium, and an arrest in the progression of ventricular compaction results in non-compaction. IVNC is usually seen in left ventricle, but both ventricle and septum can be affected as well. Previously, right ventricular (RV) non-compaction has been described only in few cases. We report a case of isolated right ventricular (RV) non-compaction diagnosed at 33weeks’ gestation. The echocardiographic study demonstrated right ventricle dilatation with abnormal muscular hypertrophy, including ventricular papillary muscle. Doppler flow patterns were normal, with no tricuspid regurgitation or ventricular septal defect and normal flow in the venous duct. This male baby was born by spontaneous vaginal delivery at 40+1 weeks gestations with Apgar scores of 9 and 10 at 1 min and 5 mins, respectively. Postnatal Echocardiography showed mild RV dilatation and hyperechogenic endocardium. The baby remained asymptomatic until 5 months of age, followed by improvement of mild RV dysfunction.