Lichen sclerosus et atrophicus (LSeA) is a benign chronic inflammatory disease that commonly occurs in prepubertal and postmenopausal women. The pathogenesis of LSeA is unknown, but genetic susceptibility, autoimmune mechanism, trauma, infection and hormonal abnormality have been suggested as etiologic factors. It is characterized by pruritic, well-demarcated, whitish sclerotic atrophic patches or plaques, predominantly located on the anogenital area. Histopathologically, it shows hyperkeratosis with atrophy in the epidermis, hyalization of the collagen bundles in papillary dermis and lymphocytic infiltrates in the reticular dermis. Treatment of LSeA includes topical corticosteroids, topical calcineurin inhibitors and intralesional steroid injections. Long-term follow-up should be considered as there is a high risk of recurrence. A 2-year-old female presented with 7-month history of spreading, hypopigmented sclerotic patches on the right anterior chest. There were no associated symptoms or history of infectious diseases and trauma. Histopathologic findings from punch biopsy specimen showed basal cell vacuolization, upper dermal edema, hyalization of collagen and adnexal inflammatory cell infiltrates in the dermis. The patient was diagnosed with lichen sclerosus et atrophicus. Herein we report a case of lichen sclerosus et atrophicus at childhood.