Posterior reversible encephalopathy syndrome (PRES) is characterized by a clinical and radiological entity with seizure, headache, hypertension, visual loss and encephalopathy with neuroimaging findings of reversible vasogenic subcortical edema. The co-morbid conditions is hypertension, renal disease, autoimmune disease, eclampsia and transplantation. A 42-year-old woman was admitted to our hospital with complaint of sudden onset of seizure. Her blood pressure is 210/110mmHg and mental is drowsy state. After this episode she compained of blindness for a few days. Brain MRI showed multifocal edema in bilateral occipital lobe, frontoparietal lobe. In several hypertensive work-up studies, renal doppler ultrasonography showed stenosis of right renal artery. Segmental stenosis in right renal artery was demonstrated by renal angiography. We performed stent insertion in renal artery narrowing portion. Her blood pressure was maintained less than 140/80mmHg without the antihypertensive drugs. PRES was induced by renal hypertension and it’s cause was right renal artery stenosis. Here we report a rare case of renal artery stnenosis with complication of PRES.