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성인에서 간혈관종에 의해 발생한 카사바-메리트 증후군
Hepatic Hemangioma with Kasabach-Merritt Syndrome in an Adult Patient
옥찬영 ( Chan Young Oak ) , 전충환 ( Chung Hwan Jun ) , 조은애 ( Eun Ae Cho ) , 이두현 ( Du Hyun Lee ) , 조성범 ( Sung Bum Cho ) , 박창환 ( Chang Hwan Park ) , 주영은 ( Young Eun Joo ) , 김현수 ( Hyun Soo Kim ) , 류종선 ( Jong Sun Rew ) , 최성규 ( Sung Kyu Choi )
UCI I410-ECN-0102-2017-510-000074500
This article is 4 pages or less.

Hemangiomas are the most common benign tumors of the liver. They are generally asymptomatic, but giant hemangiomas can lead to abdominal discomfort, bleeding, or obstructive symptoms. Kasabach-Merritt syndrome is a rare but life-threatening complication of hemangioma, characterized by consumptive coagulopathy with large vascular tumors. More than 80% of Kasabach-Merritt syndrome cases occur within the first year of life. However, there are few reports of Kasabach-Merritt syndrome with giant hepatic hemangioma in adults and, as far as we know, no reports of Kasabach-Merritt syndrome with hepatic hemangioma treated with first line medical treatment only. The most important treatment for this syndrome is removal of the large vascular tumor. However, surgical treatment entails risk of bleeding, and the patient’s condition can mitigate against surgery. We herein present a case of unresectable giant hepatic hemangioma with disseminated intravascular coagulopathy. The patient was a 60-year-old woman who complained of hematochezia, ecchymosis, and abdominal distension. She refused all surgical management and was therefore treated with systemic glucocorticoids and beta-blockers. After two weeks of steroid therapy, she responded partially to the treatment. Her laboratory findings and hematochezia improved. She was discharged on hospital day 33 and observed without signs of bleeding for three months. (Korean J Gastroenterol 2016;67:220-223)

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