Syringoid eccrine carcinoma (SEC) is a rare cutaneous malignant tumor thought to be derived from eccrine sweat apparatus. It is usually present in the head, neck and trunk region. SEC shows an infiltrative growth pattern, with deep invasion and often shows recurrences. However, metastases in the regional lymph nodes are extremely rare as are disseminated metastases. A 94-year-old male patient visited our department with an 80-year history of a lesion on his left thigh. Physical examination revealed a 2x2cm sized well-demarcated round shaped erythematous to pinkish colored nodule with ulcer on his left thigh. Histological findings from the punch biopsy of the lesion revealed that tumor consisted mainly of numerous small cords and nests from the reticular dermis extending close to subcutaneous tissue. Most of the tumor nests and cords formed luminal or tubular structures and the tumor cells showed variable atypia. Some ductal structure showed tadpole appearance and were consisted of anaplastic cell with deep basophilic nucleus. Immunohistochemical staining of cytokeratin-7, carcinoembryonic antigen and Ki-67 were reactive. Based on these findings, the final diagnosis was made as SEC. CT scan indicated a solitary lesion without metastasis. The patient was treated with local wide excision and didn’t show any recurrence during the follow-up period of 7 months. Herein, we report a very rare case of SEC which occurred on the left thigh.