Pigmented neurofibroma (PNF) is a rare variant of tumor consisting neurofibroma with melanin-laden pigmented cells. Rarely, there has been reported PNF with hypertrichosis. In that case, differential diagnoses of smooth muscle harmatoma and combined with Becker’s nevus are required. Case 1, a 29-year-old man presented with localized brownish plaque with hypertrichosis on the left side of forehead. In physical examination, 15x15cm size, well-defined brownish plaque with excessive terminal hair on the left side of forehead. On histopathologic finding, the hair follicles were abundant in the dermis and the spindle cell proliferation with wavy nuclei were detected within deep reticular dermis. Spindle cells were positive for S-100 and also showing positive to melan-A melanin-laden cells were scattered. Case 2, 7-year-girl presented with solitary palpable mass in subcutis and brownish patch with hypertrichosis on the left shin. Also on histologic exam, revealed prominent hair follicle, spindle cell proliferation and scattered melanin-laden cells were observed. Both patients, the diagnosis of PNF with hypertrichosis was made by distinctive histopathologic findings. Herein, we experience two cases of PNF with hypertrichosis. This will be helpful understanding distinctive histopathologic finding of PNF with hypertrichosis.