Granular cell tumors (GCTs) are rare and mostly benign neoplasms. They are commonly seen in the skin, tongue, breasts, and larynx. Histogenesis of GCT is uncertain, but they are reported to be neural crest origin. A 65-year-old woman presented with an asymptomatic and well-demarcated skin-colored mass on tongue. About 10 years ago, the mass developed and has gradually grown. Physical examination showed the presence of a non-tender, firm, 1 X 1cm sized dome shaped nodule. Histopathologic examination revealed an ill-defined dermal nodule composed of large cells with abundant eosinophilic granular cytoplasm. The overlying squamous epithelium showedpseudoepitheliomatous hyperplasia. Immunohistochemical stain revealed positivity for S-100 protein. Based on these findings, we diagnosed this neoplasm as GCT on the tongue.