Esophageal carcinoid tumors remain some of the rarest of all carcinoid tumors, with only several cases previously reported in the litera-ture. The endoscopic mucosal resection of selected carcinoid tumors has been shown to be a valid, safe, and effective method of treat-ment. Endoscopic ultrasonography is the technique of choice to select patients eligible for endoscopic resection. Here, we report success-ful endoscopic mucosal resection of a low esophageal carcinoid tumor and review the relevant literature. The present case is the first reported case of esophageal carcinoid tumor in Korea.