Kimura's disease is a granulomatous disease which develops in the skin, subcutaneous tissues and lymph nodes and which is characterized histologically by the presence of lymphnid follicles, vascular proliferation and infiltration with eosinophils. This disease is mostly confined to the Far East. The frequency of renal involvement in association with this disease is apparently high. But there wasn't any case report of IgA nephropathy associated with Kimura's disease. We report a case of IgA nephropathy associated with Kimura's disease with a review of the literature.