We presented a case of liver cirrhosis with the syn - drome of finger clubbing, cyanosis and polycythemia. A 48 - year - old woman was admitted to the hospital because of severe hypoxemia. On examination, finger clubbing with marked central cyanosis were noted. No cardiac murmurs were audible. The hematocrit was 60.1% and the reticulocyte count 1.9%. The arterial oxygen tension during the breathing of room air was 41 mmHg and the calculated shunt ratio (Qs/Qt) was 16.6 the had the undrelying Budd-Chiari syndrome demonstrated by inferior venacavogram. The lung funetion test revealed no evidence of obstructive or restrictive lung disease. The echocardiogram showed non-specific findings. The lung perfusion scan using Tc-MAA was compatible with the presence of the intrapulmonary shuntina.