Extrahepatic obstruction of the portal vein with resulting portal hypertension may cause extensive collateral circulation at the porta hepatis. These collateral veins may compress and narrow the common bile duct, sometimes causing obstructive jaundiee. We present a 31-year-old-male patient, in whom choledochal varix accompanied by intra-and extrahepatic stones were diagnased by Doppler ultrasonography, ERCP and angiography. ERCP demonstrated the irregular contour. of the common bile duct and multple intraluminal filling defects. We performed splenorenal shunt and then percutaneous transhepatic biliary drainage. All bile duct stones could be removed by percutaneous route.