Since Abrikossoff first reported five cases of granular celll tumor of the tongue in 1926, this tumor has been reported in many different locations throughout the body. The purpose of this paper is to discuss the clinical and pathologic features in a case of gran- ular cell tomor of the esophagus. A case of granular cell tumor of the esophagus is reported. This 36 year old female patient was admitted to the hospital because of vomiting. She was re- vealed esophageal rnass on gastrofibroscopy and demonstrated granular cell tumor in histo- pathologic examination of esophageal biopsy. (Korean J Gastroenterol 1994; 26: 327-331)