6 cases of nevus sebaceus of Jadassohn were reported and its literatures were reviewed. It is thought to be rather rare disease in this country. Two of the cases were seen within the age of 2 years and showed the clinical pictures of early stage. The remaining 4 cases were the clinical pictures of late stage showing verrucous lesions. All cases developed the lesions in the scaIp except case 6 which appeared on anterior neck. One of thc cases was associated with syringocystadenoma papilliferum but none of the cases show any association of basal cell carcinoma.