저자들은 세계적으로 드물며, 우리 나라에서도 보고된 예가 없는 후복막에 발생한 원발성 장액성 암종 1예를 경험하였기에 이를 문헌 고찰과 함께 보고하는 바이다.

Primary retroperitoneal serous carcinoma is extremely rare tumor. It is histologically identical to ovarian serous papillary carcinoma but without any evidence of ovaries, pancreas, gallbladder, appendix or abdominal origin. Histogenesis of this neoplasm remains uncertain. Ectopic ovarian tissue or coelomic metaplasia of retroperitoneal mesothelium has been proposed as its origin. We experienced a case of primary retroperitoneal serous carcinoma in an 53-year-old woman. Therefore, we present this case with a brief review of the literature.