저자들은 18세 터너증후군으로 확인된 환자에서 발생한 난소 SCTAT의 보존적 수술을 시행한 후 6년 8개월 만에 두경부, 골반부, 복부림프절의 재발 및 전이가 확인되어 BEP 병합 화학요법을 3회 시행하였다. 환자는 마지막 추적검사에서 부분적 관해를 보였으며 치료 중단 후 만 1 년이 넘은 현재에도 특이한 증상 및 불편감 없이 생활하고 있다. 이에 임상적인 문헌 고찰과 함께 보고하는 바이다.

Sex cord tumor with annular tubules (SCTAT) is an unusual ovarian neoplasm. The standard treatment for recurrent SCTAT was not established. This tumor was considered as a tumor with low-grade malignancy. A case of recurrent ovarian sex cord tumor with annular tubules in a 24-year old female with Turner`s syndrome was reported. The recurrence and metastasis were diagnosed accidentally through the operation of a palpable neck mass in the department of ENT in our hospital. Retroperitoneal lymphatic metastasis was thought to an important pathway of spread. Persistent amenorrhea, pelvic mass, and para-aortic masses were important clinical features. The patient was treated with combination chemotherapy of three cycles. The regimen consisted of bleomycin, etoposide, and cisplatin.