Rhabdomyosarcoma is one of the commonest soft tissus tumor in children. After the head and neck, genitourinary rhabdomyosarcoma is the second most common site. There are four major types of rhabdomyosarcoma: embryonal, alveolar,pleomorphic, and undir-ferentiated. A subtype of embryonal rhabdomyosarcoma is often denoted by the descrip-tive term "sarcoma botryoides", because of alayer of spimdle cells pushing up beneath the moucosa in polupoid masses. Rhabdomyosarcoma of the cervix is very rare. Simpson re-viewed 38 cases of cervical sarcoma botryoides from the world literature to 1943. Till nowa-days, total number of the cases in the literature is less than 100. Fruther experiences with a large number of cases are necessary for better management and prognosis. Recently we have experienced a case of rhabdomyosarcoma arising from the uterine cervix. This case is pre-sented with abrief review of the literature.