We experienced a cases of Angiomyolipoma of the uterus who was adimtted to our ob and gyn. Department of Obsterics and Gyunecology, the impression of the ovarian tumor of undetermined site. After laparatomy we confirmed the tumor mass was uterine tumor which was reported as angiomyolipoma through pathological examination. The angiomyolipoma is considered as benign mixed mesodermal tumor composed of the various component that is vesseles, muscles fatty tissues, elstic tissues, etc. This tumor has much rare incidence in the uterus but relatively common incidence in the kidney. We present this tumor because of its rarity and interesting pathological entity.