Multiple endocrine neoplasia (MEN) is a combination of endocrine tumor associations and consists of 3 types : 1, 2A and 2B. Herein, we report a case of insulinoma which is combined with pheochromocytoma discovered at the left adrenal gland which was treated by surgical resection. We think there is a possibility of a new type of multiple endocrine neoplasia (MEN) (J Kor Soc Endocrinol 15:640-647, 2000)