최근저자들은 임신 37주에 둔위로 제왕절개술을 시행하여 분만하였던 임신과 동반된 급성 간헐성 포피린증(AIP) 환자 1예를 경함하였기에 문헌고찰과 함께 보고하는 바이다.

The Porphyria are a group of inherited and acquired disorders characterized by partial defects in the heme biosynthetic pathway. Among the hepatic forms, acute intermittent porphyria(AIP) is the most severe and common type in western hemisphere. Though its association with pregnancy is rare, it presents the obstetrician with challenging problems in diagnosis and management and it is probable that pregnancy had some deleterious effect in acute porphyria. The authors present a cae of AIP in pregnancy with a review of literature.